Papuloerythroderma of Ofuji
| Papuloerythroderma of Ofuji |
| Classification and external resources |
| ICD-10 |
L30.8 (ILDS L30.806) |
Papuloerythroderma of Ofuji is a rare disorder most commonly found in Japan, characterized by pruritic papules that spare the skinfolds, producing bands of uninvolved cutis, creating the so-called deck-chair sign. Frequently there is associated blood eosinophilia. Skin biopsies reveal a dense lymphohistiocytic infiltrate, eosinophils in the papillary dermis, and increased Langerhans cells (S-100 positive). Systemic steroids are the treatment of choice and may result in long-term remissions.[1]:57[2]
It was characterized in 1984.[3][4]
Use of PUVA in treatment has been described.[5]
See also
References
- ^ James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN 0721629210.
- ^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
- ^ Torchia D, Miteva M, Hu S, Cohen C, Romanelli P (March 2010). "Papuloerythroderma 2009: Two New Cases and Systematic Review of the Worldwide Literature 25 Years after Its Identification by Ofuji et al". Dermatology 220 (4): 311–320. doi:10.1159/000301915. PMID 20339287. http://content.karger.com/produktedb/produkte.asp?typ=fulltext&file=000301915.
- ^ Ofuji S, Furukawa F, Miyachi Y, Ohno S (1984). "Papuloerythroderma". Dermatologica 169 (3): 125–30. PMID 6148269.
- ^ Günter Burg; Werner Kempf (2005). Cutaneous Lymphomas. Informa Health Care. pp. 365–. ISBN 9780824729974. http://books.google.com/books?id=xtm_H3u2QYAC&pg=PA365. Retrieved 30 May 2010.